Diagnostic Slide Session

American Association of Neuropathologists

O.T. Bailey-Helena Riggs Award (2005 - present)

 

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Year

Recipient

Institution

Case (with links)

2023

 

 

Cassie B. MacRae, MD

 

Best Neurodegenerative Case: Anfisa Baiandurova, MD; Randy Woltjer, MD, PhD

 

Best Neurodegenerative Case, Honorable Mention: M. Adelita Vizcaino, MD; Divyanshu Dubey, MBBS; R. Ross Reichard, MD

Bringham and Women's Hospital

 

Oregon Health & Science University

 

 

Mayo Clinic

Dura with dense acute & chronic inflammation and immuno-positive/Whartin-Starry positive Spirochetes c/w Treponema pallidum - Syphilis

 

Beta-propeller protein-associated neurodegeneration (BPAN)

 

 

Anti-IgLON5-related disease

2022

Antony Tuzzolo, MD; Jesse Lee Kresak, MD

 

Honorable Mention: Angus Toland, MD; Donald Born, MD, PhD

Best Neurodegenerative Case: Bryan Morales-Vargas, MD; Steward Neil, MD; Marla Gearing, PhD; Matthew Schniederjan, MD

Best Neurodegenerative Case, Honorable Mention: Tiffany Baker, MD, PhD

University of Florida

 

 

Stanford Medicine

 

Emory University School of Medicine

 

Medical University of South Carolina

Atypical lymphoplasmacytic infiltrate of the choroid plexus with background xanthogranulomatous reaction, consistent with marginal zone B-cell lymphoma

 

CIC – rearranged sarcoma

 

Fragile X – associated tremor ataxia syndrome (FXTAS)

 

Galloway-Mowat syndrome (GAMOS)

 2021

Thomas Zaikos, MD, PhD; Jason Savell, MD; Fausto Rodriguez, MD; Meaghan Morris, MD, PhD; Peter Burger, MD

Honorable Mention: Lorraina J. Robinson, DO, MS; Christian Davidson, MD; Joshua M. Klonoski, MD, PhD; Eric A. Goold, MD

Best Neurodegenerative Case: Kathryn Eschbacher, MD, Eleni Constantopoulos, MHS, PA(ASCP), and Aivi Nguyen, MD

Johns Hopkins Medicine

 

 

 

 

University of Utah Health

 

 

 

 

Mayo Clinic, Rochester, MN

Chronic inflammation and JC virus granule cell neuronopathy

 

 

 

 

Microangiopathic leukoencephalopathy associated with COL4A1 mutation

 

 

 

Neuronal intranuclear inclusion disease. Lew body disease, limbic (transitional) type.

2020

M. Adelita Vizcaino

Best Neurodegenerative Case:
Lucy Evans

Mayo Clinic Rochester, MD

University of Iowa

Angiomatoid fibrous histiocytoma with rhabdoid features 

Juvenile neuronal ceroid lipofuscinosis/CLN3 disease (Batten Disease)

2019

Emily Sloan



Best Neurodegenerative Case:
 
Julieann C. Lee

University of California - San Francisco


University of California - San Francisco

 

Donor-derived glioneuronal proliferation following intrathecal stem cell injection


Neurodegeneration with features of a neuroferritinopathy

2018

Jason A. Gregory

 

Best Neurodegenerative Cases:  
Anne Shepler
Aivi Nguyen

University of Florida

 

University of Pittsburgh
University of Pennsylvania


Glioneuronal hamartomatous proliferation of the brainstem in a patient with fibrodysplasia ossificans progressiva

Basophilic inclusion body disease
Progressive supranuclear palsy (PSP) with 4R-tau positive Pick body-like inclusions

 

2017

Drew Williamson


Honorable Mention:
  Andrew R. Guajardo

University Hospitals Cleveland Medical Center

Johns Hopkins University

Cortical Dysplasia (radiation-induced)


Dyskeratosis Congenita, Hoyeraal-Hreidarsson Variant

 

2016

Elaine S. Keung

Walter Reed National Military Medical Center

Chondroid Lipoma

2015

Phedias Diamandis, MD

University of Toronto

Malignant fat-forming solitary fibrous tumor

2014

Matthew D. Cykowski

Baylor College of Medicine

Chagas disease; trypanosomiasis

2013

Gerald Reis

University of California, San Francisco

Cerebromeningeal hemophagocytic lymphohistiocytosis

2012

Joshua Menke

Mayo Clinic, Rochester, MN

Toxic spongiform leukoencephalopathy

2011

Pedro Ciarlini

University Hospitals Case Medical Center

Necrotizing eosinophilic meningoencephalitis

2010

Sriram Venneti

University of Pennsylvania

Epithelial and spindle (sarcomatous) and chondroid (mesenchymal) elements

2009

Craig Horbinski

University of Pittsburgh

Inflammatory pseudotumor in a patient with serum anti-aquaporin-4 antibody (neuromyelitis optica, or Devic's disease)

2008

Gabrielle Yeaney

University of Pittsburgh

Diffuse malignant Schwannian leptomeningeal sarcomatosis

 

2007

C. Dirk Keene

University of Washington

Viable fetal neural tissue grafts with associated marked gliosis

 

2006

Lili-Nazna Hazrati

University of Toronto

Desmoplastic infantile ganglioglioma

 

2005

Kathryn McFadden

University of Pittsburgh

Neuronal intranuclear inclusion disease (NIID), juvenile-sporadic

 

 

 
(Drs. Rebecca Folkerth, Betty Kleinscmidt-DeMasters, Tejus Bale, Caterina Giannini)